Neonatal and adolescent paratesticular rhabdomyosarcoma (Publication presentation)

Abstract

Background/Objectives: Paratesticular rhabdomyosarcoma (PTRMS) accounts for only 12% of childhood scrotal tumours. We report an exceedingly rare presentation in a neonate and evaluate the disease free survival and overall survival in patients with PTRMS. Design/Methods: We retrospectively reviewed all paediatric surgical patients with PTRMS in our centre from 2000 to 2019. Results: Two patients (aged 0 day and 17 years at presentation) with non‐metastatic PTRMS were identified. Both underwent unilateral inguinal orchidectomy revealing embryonal histology. In the neonate, local invasion to the paratesticular fat was found requiring left hemiscrotectomy. Surgical resection was complete in both patients. None underwent lymph node sampling, retroperitoneal lymph node dissection or radiotherapy. No complications from chemotherapy were reported. Disease free survival and overall survival were 100%. Follow up duration was 3 years and 19 years respectively. Conclusions: Paratesticular rhabdomyosarcoma can arise in neonates and are completely asymptomatic. Prompt recognition, referral to a specialized centre and adequate surgery is essential. The long term disease free and survival outcome are excellent in non‐metastatic PTRMS.