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Article: A Single Center Experience of Primary Immunodeficiencies in Hong Kong
Title | A Single Center Experience of Primary Immunodeficiencies in Hong Kong |
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Authors | |
Keywords | Bone marrow transplant Infection Lymphoma Primary immunodeficiencies |
Issue Date | 1999 |
Publisher | Medcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.asp |
Citation | Hong Kong Journal of Paediatrics (New series), 1999, v. 4, p. 16-20 How to Cite? |
Abstract | A total of 99 cases of primary immunodeficiency diseases (PID) (61 males, 38 females) were registered at the Paediatric Immunology Clinic, Queen Mary Hospital, University of Hong Kong between July, 1988 and December, 1998. The following frequencies were found: predominantly humoral defects (n=34); predominantly T cell defects (n=15); combined immunodeficiency (n=5); phagocytic disorders (n=35); others (n=10). Chronic neutropenia was the most frequent disorder (n= 19), followed by X-linked agammaglobulinemia (n= 12), chronic granulomatous disease (n=12), selective deficiency of IgG subclass (n=10), common variable immunodeficiency (n=7), Wiskott-Aldrich syndrome (n=6) and severe combined immunodeficiency (n=5). Infection was the major complication leading to mortality (n=6). Lymphoma developed in 3 patients. Bone marrow transplantation was done in 12 patients with over 90% success rate. The clinical approach and general principles of management of PIDs will also be discussed. |
Persistent Identifier | http://hdl.handle.net/10722/79872 |
ISSN | 2023 Impact Factor: 0.1 2023 SCImago Journal Rankings: 0.117 |
DC Field | Value | Language |
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dc.contributor.author | Lee, TL | - |
dc.contributor.author | Chan, GCF | - |
dc.contributor.author | Ha, SY | - |
dc.contributor.author | Lau, YL | - |
dc.date.accessioned | 2010-09-06T07:59:42Z | - |
dc.date.available | 2010-09-06T07:59:42Z | - |
dc.date.issued | 1999 | - |
dc.identifier.citation | Hong Kong Journal of Paediatrics (New series), 1999, v. 4, p. 16-20 | - |
dc.identifier.issn | 1013-9923 | - |
dc.identifier.uri | http://hdl.handle.net/10722/79872 | - |
dc.description.abstract | A total of 99 cases of primary immunodeficiency diseases (PID) (61 males, 38 females) were registered at the Paediatric Immunology Clinic, Queen Mary Hospital, University of Hong Kong between July, 1988 and December, 1998. The following frequencies were found: predominantly humoral defects (n=34); predominantly T cell defects (n=15); combined immunodeficiency (n=5); phagocytic disorders (n=35); others (n=10). Chronic neutropenia was the most frequent disorder (n= 19), followed by X-linked agammaglobulinemia (n= 12), chronic granulomatous disease (n=12), selective deficiency of IgG subclass (n=10), common variable immunodeficiency (n=7), Wiskott-Aldrich syndrome (n=6) and severe combined immunodeficiency (n=5). Infection was the major complication leading to mortality (n=6). Lymphoma developed in 3 patients. Bone marrow transplantation was done in 12 patients with over 90% success rate. The clinical approach and general principles of management of PIDs will also be discussed. | - |
dc.language | eng | - |
dc.publisher | Medcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.asp | - |
dc.relation.ispartof | Hong Kong Journal of Paediatrics (New series) | - |
dc.subject | Bone marrow transplant | - |
dc.subject | Infection | - |
dc.subject | Lymphoma | - |
dc.subject | Primary immunodeficiencies | - |
dc.title | A Single Center Experience of Primary Immunodeficiencies in Hong Kong | - |
dc.type | Article | - |
dc.identifier.openurl | http://library.hku.hk:4550/resserv?sid=HKU:IR&issn=1013-9923&volume=4&spage=16&epage=20&date=1999&atitle=A+Single+Center+Experience+of+Primary+Immunodeficiencies+in+Hong+Kong | en_HK |
dc.identifier.email | Chan, GCF: gcfchan@hkucc.hku.hk | - |
dc.identifier.email | Ha, SY: syha@hkucc.hku.hk | - |
dc.identifier.email | Lau, YL: lauylung@hkucc.hku.hk | - |
dc.identifier.authority | Chan, GCF=rp00431 | - |
dc.identifier.authority | Lau, YL=rp00361 | - |
dc.description.nature | link_to_OA_fulltext | - |
dc.identifier.hkuros | 40589 | - |
dc.identifier.volume | 4 | - |
dc.identifier.spage | 16 | - |
dc.identifier.epage | 20 | - |
dc.publisher.place | Hong Kong | - |
dc.identifier.issnl | 1013-9923 | - |