Article: Identification and characterization of EBP, a novel EEN binding protein that inhibits Ras signaling and is recruited into the nucleus by the MLL-EEN fusion protein
| Title | Identification and characterization of EBP, a novel EEN binding protein that inhibits Ras signaling and is recruited into the nucleus by the MLL-EEN fusion protein |
|---|---|
| Authors | Yam, JWP Jin, DY So, CW Chan, LC1 |
| Keywords | Carrier Proteins - chemistry - genetics - metabolism DNA-Binding Proteins - genetics - metabolism Nucleocytoplasmic Transport Proteins Proto-Oncogenes Steroid Isomerases |
| Issue Date | 2004 |
| Publisher | American Society of Hematology. The Journal's web site is located at http://bloodjournal.hematologylibrary.org/ |
| Citation | Blood, 2004, v. 103 n. 4, p. 1445-1453 [How to Cite?] DOI: http://dx.doi.org/10.1182/blood-2003-07-2452 |
| Abstract | The chimeric MLL-EEN fusion protein is created as a result of chromosomal translocation t(11;19)(q23;p13). EEN, an Src homology 3 (SH3) domain-containing protein in the endophilin family, has been implicated in endocytosis, although little is known about its role in leukemogenesis mediated by the MLL-EEN fusion protein. In this study, we have identified and characterized EBP, a novel EEN binding protein that interacts with the SH3 domain of EEN through a proline-rich motif PPERP. EBP is a ubiquitous protein that is normally expressed in the cytoplasm but is recruited to the nucleus by MLL-EEN with a punctate localization pattern characteristic of the MLL chimeric proteins. EBP interacts simultaneously with EEN and Sos, a guanine-nucleotide exchange factor for Ras. Coexpressoin of EBP with EEN leads to suppression of Ras-induced cellular transformation and Ras-mediated activation of Elk-1. Taken together, our findings suggest a new mechanism for MLL-EEN-mediated leukemogenesis in which MLL-EEN interferes with the Ras-suppressing activities of EBP through direct interaction. © 2004 by The American Society of Hematology. |
| ISSN | 0006-4971 2011 Impact Factor: 9.898 2011 SCImago Journal Rankings: 1.698 |
| DOI | http://dx.doi.org/10.1182/blood-2003-07-2452 |
| ISI Accession Number ID | WOS:000188828200046 |
| References | References in Scopus |
| dc.contributor.author | Yam, JWP |
|---|---|
| dc.contributor.author | Jin, DY |
| dc.contributor.author | So, CW |
| dc.contributor.author | Chan, LC |
| dc.date.accessioned | 2008-05-22T04:15:24Z |
| dc.date.available | 2008-05-22T04:15:24Z |
| dc.date.issued | 2004 |
| dc.description.abstract | The chimeric MLL-EEN fusion protein is created as a result of chromosomal translocation t(11;19)(q23;p13). EEN, an Src homology 3 (SH3) domain-containing protein in the endophilin family, has been implicated in endocytosis, although little is known about its role in leukemogenesis mediated by the MLL-EEN fusion protein. In this study, we have identified and characterized EBP, a novel EEN binding protein that interacts with the SH3 domain of EEN through a proline-rich motif PPERP. EBP is a ubiquitous protein that is normally expressed in the cytoplasm but is recruited to the nucleus by MLL-EEN with a punctate localization pattern characteristic of the MLL chimeric proteins. EBP interacts simultaneously with EEN and Sos, a guanine-nucleotide exchange factor for Ras. Coexpressoin of EBP with EEN leads to suppression of Ras-induced cellular transformation and Ras-mediated activation of Elk-1. Taken together, our findings suggest a new mechanism for MLL-EEN-mediated leukemogenesis in which MLL-EEN interferes with the Ras-suppressing activities of EBP through direct interaction. © 2004 by The American Society of Hematology. |
| dc.description.nature | postprint |
| dc.format.extent | 146861 bytes |
| dc.format.extent | 3021 bytes |
| dc.format.mimetype | application/pdf |
| dc.format.mimetype | text/plain |
| dc.identifier.citation | Blood, 2004, v. 103 n. 4, p. 1445-1453 [How to Cite?] DOI: http://dx.doi.org/10.1182/blood-2003-07-2452 |
| dc.identifier.doi | http://dx.doi.org/10.1182/blood-2003-07-2452 |
| dc.identifier.epage | 1453 |
| dc.identifier.hkuros | 86076 |
| dc.identifier.isi | WOS:000188828200046 |
| dc.identifier.issn | 0006-4971 2011 Impact Factor: 9.898 2011 SCImago Journal Rankings: 1.698 |
| dc.identifier.issue | 4 |
| dc.identifier.openurl | ![]() |
| dc.identifier.pmid | 14551139 |
| dc.identifier.scopus | eid_2-s2.0-0842307321 |
| dc.identifier.spage | 1445 |
| dc.identifier.uri | http://hdl.handle.net/10722/48499 |
| dc.identifier.volume | 103 |
| dc.language | eng |
| dc.publisher | American Society of Hematology. The Journal's web site is located at http://bloodjournal.hematologylibrary.org/ |
| dc.publisher.place | United States |
| dc.relation.ispartof | Blood |
| dc.relation.references | References in Scopus |
| dc.rights | Creative Commons: Attribution 3.0 Hong Kong License |
| dc.subject | Carrier Proteins - chemistry - genetics - metabolism |
| dc.subject | DNA-Binding Proteins - genetics - metabolism |
| dc.subject | Nucleocytoplasmic Transport Proteins |
| dc.subject | Proto-Oncogenes |
| dc.subject | Steroid Isomerases |
| dc.title | Identification and characterization of EBP, a novel EEN binding protein that inhibits Ras signaling and is recruited into the nucleus by the MLL-EEN fusion protein |
| dc.type | Article |
Author Affiliations
- Queen Mary Hospital Hong Kong


