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Article: Retrospective review on anomalous left coronary artery from pulmonary artery

TitleRetrospective review on anomalous left coronary artery from pulmonary artery
Authors
KeywordsAnomalous left coronary artery from pulmonary artery
Diagnosis
Presentation
Surgical outcomes
Issue Date2010
PublisherMedcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.asp
Citation
Hong Kong Journal Of Paediatrics, 2010, v. 15 n. 1, p. 12-18 How to Cite?
AbstractAnomalous left coronary artery from pulmonary artery (ALCAPA) is a rare but important congenital coronary anomaly. Patients with ALCAPA typically present with paroxysms of crying, pallor, diaphoresis, agitation and heart failure in infancy due to myocardial ischaemia. Clinical course thus very much depends on the presence and development of collateral circulation. We report the clinical presentation and method of diagnosis of ALCAPA in Chinese children in Hong Kong. We also study their long term outcomes after surgery and compare local data with overseas results. Early diagnosis and correction are important to avoid development of or progression of mitral regurgitation, which appeared to be associated with lower chance of requiring mitral valve annuloplasty/replacement. The majority of patients in Hong Kong presents as infantile form with heart failure, mitral regurgitation and dilated cardiomyopathy. Typical ECG changes are present in 5 cases (55.6%). Echocardiography confirms the diagnosis in 3 cases (33.3%). The remaining patients require cardiac catheterization to confirm the diagnosis. Early diagnosis therefore relies on a high index of suspicion. The diagnosis of ALCAPA should be considered as differential diagnosis of mitral regurgitation, endocardial fibroelastosis and dilated cardiomyopathy. Cardiac catheterization is warranted in doubtful cases. Long-term survival and outcome after surgical treatment appear to be favourable with good functional status. Residual lesions occur in 4 (44.4%) patients and re-operation on the mitral valve is required in 1 (11.1%) patient. Our local results are comparable to overseas reports.
Persistent Identifierhttp://hdl.handle.net/10722/130949
ISSN
2014 Impact Factor: 0.133
2014 SCImago Journal Rankings: 0.126
References

 

DC FieldValueLanguage
dc.contributor.authorKo, LYen_HK
dc.contributor.authorChau, AKTen_HK
dc.contributor.authorYung, TCen_HK
dc.contributor.authorCheung, YFen_HK
dc.contributor.authorLun, KSen_HK
dc.date.accessioned2011-01-07T09:16:08Z-
dc.date.available2011-01-07T09:16:08Z-
dc.date.issued2010en_HK
dc.identifier.citationHong Kong Journal Of Paediatrics, 2010, v. 15 n. 1, p. 12-18en_HK
dc.identifier.issn1013-9923en_HK
dc.identifier.urihttp://hdl.handle.net/10722/130949-
dc.description.abstractAnomalous left coronary artery from pulmonary artery (ALCAPA) is a rare but important congenital coronary anomaly. Patients with ALCAPA typically present with paroxysms of crying, pallor, diaphoresis, agitation and heart failure in infancy due to myocardial ischaemia. Clinical course thus very much depends on the presence and development of collateral circulation. We report the clinical presentation and method of diagnosis of ALCAPA in Chinese children in Hong Kong. We also study their long term outcomes after surgery and compare local data with overseas results. Early diagnosis and correction are important to avoid development of or progression of mitral regurgitation, which appeared to be associated with lower chance of requiring mitral valve annuloplasty/replacement. The majority of patients in Hong Kong presents as infantile form with heart failure, mitral regurgitation and dilated cardiomyopathy. Typical ECG changes are present in 5 cases (55.6%). Echocardiography confirms the diagnosis in 3 cases (33.3%). The remaining patients require cardiac catheterization to confirm the diagnosis. Early diagnosis therefore relies on a high index of suspicion. The diagnosis of ALCAPA should be considered as differential diagnosis of mitral regurgitation, endocardial fibroelastosis and dilated cardiomyopathy. Cardiac catheterization is warranted in doubtful cases. Long-term survival and outcome after surgical treatment appear to be favourable with good functional status. Residual lesions occur in 4 (44.4%) patients and re-operation on the mitral valve is required in 1 (11.1%) patient. Our local results are comparable to overseas reports.en_HK
dc.languageeng-
dc.publisherMedcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.aspen_HK
dc.relation.ispartofHong Kong Journal of Paediatricsen_HK
dc.rightsDOAJ-
dc.subjectAnomalous left coronary artery from pulmonary arteryen_HK
dc.subjectDiagnosisen_HK
dc.subjectPresentationen_HK
dc.subjectSurgical outcomesen_HK
dc.titleRetrospective review on anomalous left coronary artery from pulmonary arteryen_HK
dc.typeArticleen_HK
dc.identifier.openurlhttp://library.hku.hk:4550/resserv?sid=HKU:IR&issn=1013-9923&volume=15&issue=1&spage=12&epage=18&date=2010&atitle=Retrospective+review+on+anomalous+left+coronary+artery+from+pulmonary+artery-
dc.identifier.emailCheung, YF:xfcheung@hku.hken_HK
dc.identifier.authorityCheung, YF=rp00382en_HK
dc.description.naturelink_to_OA_fulltext-
dc.identifier.scopuseid_2-s2.0-77449110803en_HK
dc.identifier.hkuros168664-
dc.relation.referenceshttp://www.scopus.com/mlt/select.url?eid=2-s2.0-77449110803&selection=ref&src=s&origin=recordpageen_HK
dc.identifier.volume15en_HK
dc.identifier.issue1en_HK
dc.identifier.spage12en_HK
dc.identifier.epage18en_HK
dc.publisher.placeHong Kongen_HK
dc.identifier.scopusauthoridKo, LY=35787212400en_HK
dc.identifier.scopusauthoridChau, AKT=35787094400en_HK
dc.identifier.scopusauthoridYung, TC=9132842300en_HK
dc.identifier.scopusauthoridCheung, YF=7202111067en_HK
dc.identifier.scopusauthoridLun, KS=8363663600en_HK

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