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Article: A Single Center Experience of Primary Immunodeficiencies in Hong Kong

TitleA Single Center Experience of Primary Immunodeficiencies in Hong Kong
Authors
KeywordsBone marrow transplant
Infection
Lymphoma
Primary immunodeficiencies
Issue Date1999
PublisherMedcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.asp
Citation
Hong Kong Journal of Paediatrics (New series), 1999, v. 4, p. 16-20 How to Cite?
AbstractA total of 99 cases of primary immunodeficiency diseases (PID) (61 males, 38 females) were registered at the Paediatric Immunology Clinic, Queen Mary Hospital, University of Hong Kong between July, 1988 and December, 1998. The following frequencies were found: predominantly humoral defects (n=34); predominantly T cell defects (n=15); combined immunodeficiency (n=5); phagocytic disorders (n=35); others (n=10). Chronic neutropenia was the most frequent disorder (n= 19), followed by X-linked agammaglobulinemia (n= 12), chronic granulomatous disease (n=12), selective deficiency of IgG subclass (n=10), common variable immunodeficiency (n=7), Wiskott-Aldrich syndrome (n=6) and severe combined immunodeficiency (n=5). Infection was the major complication leading to mortality (n=6). Lymphoma developed in 3 patients. Bone marrow transplantation was done in 12 patients with over 90% success rate. The clinical approach and general principles of management of PIDs will also be discussed.
Persistent Identifierhttp://hdl.handle.net/10722/79872
ISSN
2015 Impact Factor: 0.194
2015 SCImago Journal Rankings: 0.123

 

DC FieldValueLanguage
dc.contributor.authorLee, TL-
dc.contributor.authorChan, GCF-
dc.contributor.authorHa, SY-
dc.contributor.authorLau, YL-
dc.date.accessioned2010-09-06T07:59:42Z-
dc.date.available2010-09-06T07:59:42Z-
dc.date.issued1999-
dc.identifier.citationHong Kong Journal of Paediatrics (New series), 1999, v. 4, p. 16-20-
dc.identifier.issn1013-9923-
dc.identifier.urihttp://hdl.handle.net/10722/79872-
dc.description.abstractA total of 99 cases of primary immunodeficiency diseases (PID) (61 males, 38 females) were registered at the Paediatric Immunology Clinic, Queen Mary Hospital, University of Hong Kong between July, 1988 and December, 1998. The following frequencies were found: predominantly humoral defects (n=34); predominantly T cell defects (n=15); combined immunodeficiency (n=5); phagocytic disorders (n=35); others (n=10). Chronic neutropenia was the most frequent disorder (n= 19), followed by X-linked agammaglobulinemia (n= 12), chronic granulomatous disease (n=12), selective deficiency of IgG subclass (n=10), common variable immunodeficiency (n=7), Wiskott-Aldrich syndrome (n=6) and severe combined immunodeficiency (n=5). Infection was the major complication leading to mortality (n=6). Lymphoma developed in 3 patients. Bone marrow transplantation was done in 12 patients with over 90% success rate. The clinical approach and general principles of management of PIDs will also be discussed.-
dc.languageeng-
dc.publisherMedcom Limited. The Journal's web site is located at http://www.hkjpaed.org/index.asp-
dc.relation.ispartofHong Kong Journal of Paediatrics (New series)-
dc.subjectBone marrow transplant-
dc.subjectInfection-
dc.subjectLymphoma-
dc.subjectPrimary immunodeficiencies-
dc.titleA Single Center Experience of Primary Immunodeficiencies in Hong Kong-
dc.typeArticle-
dc.identifier.openurlhttp://library.hku.hk:4550/resserv?sid=HKU:IR&issn=1013-9923&volume=4&spage=16&epage=20&date=1999&atitle=A+Single+Center+Experience+of+Primary+Immunodeficiencies+in+Hong+Kongen_HK
dc.identifier.emailChan, GCF: gcfchan@hkucc.hku.hk-
dc.identifier.emailHa, SY: syha@hkucc.hku.hk-
dc.identifier.emailLau, YL: lauylung@hkucc.hku.hk-
dc.identifier.authorityChan, GCF=rp00431-
dc.identifier.authorityLau, YL=rp00361-
dc.description.naturelink_to_OA_fulltext-
dc.identifier.hkuros40589-
dc.identifier.volume4-
dc.identifier.spage16-
dc.identifier.epage20-
dc.publisher.placeHong Kong-

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