Article: The kinase LRRK2 is a regulator of the transcription factor NFAT that modulates the severity of inflammatory bowel disease
| Title | The kinase LRRK2 is a regulator of the transcription factor NFAT that modulates the severity of inflammatory bowel disease |
|---|---|
| Authors | Liu, Z2 Lee, J2 Krummey, S2 Lu, W2 Cai, H1 Lenardo, MJ2 |
| Issue Date | 2011 |
| Publisher | Nature Publishing Group. The Journal's web site is located at http://www.nature.com/ni |
| Citation | Nature Immunology, 2011, v. 12 n. 11, p. 1063-1070 [How to Cite?] DOI: http://dx.doi.org/10.1038/ni.2113 |
| Abstract | Leucine-rich repeat kinase 2 (LRRK2) has been identified by genome-wide association studies as being encoded by a major susceptibility gene for Crohn's disease. Here we found that LRRK2 deficiency conferred enhanced susceptibility to experimental colitis in mice. Mechanistic studies showed that LRRK2 was a potent negative regulator of the transcription factor NFAT and was a component of a complex that included the large noncoding RNA NRON (an NFAT repressor). Furthermore, the risk-associated allele encoding LRRK2 Met2397 identified by a genome-wide association study for Crohn's disease resulted in less LRRK2 protein post-translationally. Severe colitis in LRRK2-deficient mice was associated with enhanced nuclear localization of NFAT1. Thus, our study defines a new step in the control of NFAT activation that involves an immunoregulatory function of LRRK2 and has important implications for inflammatory bowel disease. © 2011 Nature America, Inc. All rights reserved. |
| ISSN | 1529-2908 2011 Impact Factor: 26.008 2011 SCImago Journal Rankings: 6.226 |
| DOI | http://dx.doi.org/10.1038/ni.2113 |
| References | References in Scopus |
| dc.contributor.author | Liu, Z |
|---|---|
| dc.contributor.author | Lee, J |
| dc.contributor.author | Krummey, S |
| dc.contributor.author | Lu, W |
| dc.contributor.author | Cai, H |
| dc.contributor.author | Lenardo, MJ |
| dc.date.accessioned | 2012-10-08T03:20:58Z |
| dc.date.available | 2012-10-08T03:20:58Z |
| dc.date.issued | 2011 |
| dc.description.abstract | Leucine-rich repeat kinase 2 (LRRK2) has been identified by genome-wide association studies as being encoded by a major susceptibility gene for Crohn's disease. Here we found that LRRK2 deficiency conferred enhanced susceptibility to experimental colitis in mice. Mechanistic studies showed that LRRK2 was a potent negative regulator of the transcription factor NFAT and was a component of a complex that included the large noncoding RNA NRON (an NFAT repressor). Furthermore, the risk-associated allele encoding LRRK2 Met2397 identified by a genome-wide association study for Crohn's disease resulted in less LRRK2 protein post-translationally. Severe colitis in LRRK2-deficient mice was associated with enhanced nuclear localization of NFAT1. Thus, our study defines a new step in the control of NFAT activation that involves an immunoregulatory function of LRRK2 and has important implications for inflammatory bowel disease. © 2011 Nature America, Inc. All rights reserved. |
| dc.description.nature | Link_to_subscribed_fulltext |
| dc.identifier.citation | Nature Immunology, 2011, v. 12 n. 11, p. 1063-1070 [How to Cite?] DOI: http://dx.doi.org/10.1038/ni.2113 |
| dc.identifier.citeulike | 9895048 |
| dc.identifier.doi | http://dx.doi.org/10.1038/ni.2113 |
| dc.identifier.epage | 1070 |
| dc.identifier.issn | 1529-2908 2011 Impact Factor: 26.008 2011 SCImago Journal Rankings: 6.226 |
| dc.identifier.issue | 11 |
| dc.identifier.pmid | 21983832 |
| dc.identifier.scopus | eid_2-s2.0-80054933395 |
| dc.identifier.spage | 1063 |
| dc.identifier.uri | http://hdl.handle.net/10722/168577 |
| dc.identifier.volume | 12 |
| dc.language | eng |
| dc.publisher | Nature Publishing Group. The Journal's web site is located at http://www.nature.com/ni |
| dc.publisher.place | United States |
| dc.relation.ispartof | Nature Immunology |
| dc.relation.references | References in Scopus |
| dc.subject.mesh | Active Transport, Cell Nucleus |
| dc.subject.mesh | Animals |
| dc.subject.mesh | Cell Line |
| dc.subject.mesh | Cell Nucleus - Metabolism |
| dc.subject.mesh | Colitis - Chemically Induced - Genetics - Immunology - Metabolism |
| dc.subject.mesh | Crohn Disease - Genetics |
| dc.subject.mesh | Disease Models, Animal |
| dc.subject.mesh | Genetic Predisposition To Disease |
| dc.subject.mesh | Humans |
| dc.subject.mesh | Macrophage Activation - Genetics |
| dc.subject.mesh | Mice |
| dc.subject.mesh | Mice, Inbred C57bl |
| dc.subject.mesh | Mice, Knockout |
| dc.subject.mesh | Nfatc Transcription Factors - Metabolism |
| dc.subject.mesh | Protein Processing, Post-Translational - Immunology |
| dc.subject.mesh | Protein-Serine-Threonine Kinases - Genetics - Metabolism |
| dc.subject.mesh | Rna, Untranslated - Metabolism |
| dc.subject.mesh | Transgenes - Genetics |
| dc.title | The kinase LRRK2 is a regulator of the transcription factor NFAT that modulates the severity of inflammatory bowel disease |
| dc.type | Article |
Author Affiliations
- National Institute on Aging
- National Institute of Allergy and Infectious Diseases

