Article: Activated oncogenic pathways and therapeutic targets in extranodal nasal-type NK/T cell lymphoma revealed by gene expression profiling
| Title | Activated oncogenic pathways and therapeutic targets in extranodal nasal-type NK/T cell lymphoma revealed by gene expression profiling |
|---|---|
| Authors | Ng, SB1 Selvarajan, V1 Huang, G6 Zhou, J6 Feldman, AL2 Law, M2 Kwong, YL5 Shimizu, N7 Kagami, Y4 Aozasa, K3 SaltoTellez, M1 6 Chng, WJ6 |
| Issue Date | 2011 |
| Publisher | John Wiley & Sons. The Journal's web site is located at http://www3.interscience.wiley.com/cgi-bin/jhome/1130 |
| Citation | Journal Of Pathology, 2011, v. 223 n. 4, p. 496-510 [How to Cite?] DOI: http://dx.doi.org/10.1002/path.2823 |
| Abstract | We performed comprehensive genome-wide gene expression profiling (GEP) of extranodal nasal-type natural killer/T-cell lymphoma (NKTL) using formalin-fixed, paraffin-embedded tissue (n = 9) and NK cell lines (n = 5) in comparison with normal NK cells, with the objective of understanding the oncogenic pathways involved in the pathogenesis of NKTL and to identify potential therapeutic targets. Pathway and network analysis of genes differentially expressed between NKTL and normal NK cells revealed significant enrichment for cell cycle-related genes and pathways, such as PLK1, CDK1, and Aurora-A. Furthermore, our results demonstrated a pro-proliferative and anti-apoptotic phenotype in NKTL characterized by activation of Myc and nuclear factor kappa B (NF-κB), and deregulation of p53. In corroboration with GEP findings, a significant percentage of NKTLs (n = 33) overexpressed c-Myc (45.4%), p53 (87.9%), and NF-κB p50 (67.7%) on immunohistochemistry using a tissue microarray containing 33 NKTL samples. Notably, overexpression of survivin was observed in 97% of cases. Based on our findings, we propose a model of NKTL pathogenesis where deregulation of p53 together with activation of Myc and NF-κB, possibly driven by EBV LMP-1, results in the cumulative up-regulation of survivin. Down-regulation of survivin with Terameprocol (EM-1421, a survivin inhibitor) results in reduced cell viability and increased apoptosis in tumour cells, suggesting that targeting survivin may be a potential novel therapeutic strategy in NKTL. © 2011 Pathological Society of Great Britain and Ireland. Published by John Wiley & Sons, Ltd. |
| ISSN | 0022-3417 2011 Impact Factor: 6.318 2011 SCImago Journal Rankings: 0.946 |
| DOI | http://dx.doi.org/10.1002/path.2823 |
| References | References in Scopus |
| dc.contributor.author | Ng, SB |
|---|---|
| dc.contributor.author | Selvarajan, V |
| dc.contributor.author | Huang, G |
| dc.contributor.author | Zhou, J |
| dc.contributor.author | Feldman, AL |
| dc.contributor.author | Law, M |
| dc.contributor.author | Kwong, YL |
| dc.contributor.author | Shimizu, N |
| dc.contributor.author | Kagami, Y |
| dc.contributor.author | Aozasa, K |
| dc.contributor.author | SaltoTellez, M |
| dc.contributor.author | Chng, WJ |
| dc.date.accessioned | 2012-09-05T05:30:33Z |
| dc.date.available | 2012-09-05T05:30:33Z |
| dc.date.issued | 2011 |
| dc.description.abstract | We performed comprehensive genome-wide gene expression profiling (GEP) of extranodal nasal-type natural killer/T-cell lymphoma (NKTL) using formalin-fixed, paraffin-embedded tissue (n = 9) and NK cell lines (n = 5) in comparison with normal NK cells, with the objective of understanding the oncogenic pathways involved in the pathogenesis of NKTL and to identify potential therapeutic targets. Pathway and network analysis of genes differentially expressed between NKTL and normal NK cells revealed significant enrichment for cell cycle-related genes and pathways, such as PLK1, CDK1, and Aurora-A. Furthermore, our results demonstrated a pro-proliferative and anti-apoptotic phenotype in NKTL characterized by activation of Myc and nuclear factor kappa B (NF-κB), and deregulation of p53. In corroboration with GEP findings, a significant percentage of NKTLs (n = 33) overexpressed c-Myc (45.4%), p53 (87.9%), and NF-κB p50 (67.7%) on immunohistochemistry using a tissue microarray containing 33 NKTL samples. Notably, overexpression of survivin was observed in 97% of cases. Based on our findings, we propose a model of NKTL pathogenesis where deregulation of p53 together with activation of Myc and NF-κB, possibly driven by EBV LMP-1, results in the cumulative up-regulation of survivin. Down-regulation of survivin with Terameprocol (EM-1421, a survivin inhibitor) results in reduced cell viability and increased apoptosis in tumour cells, suggesting that targeting survivin may be a potential novel therapeutic strategy in NKTL. © 2011 Pathological Society of Great Britain and Ireland. Published by John Wiley & Sons, Ltd. |
| dc.description.nature | Link_to_subscribed_fulltext |
| dc.identifier.citation | Journal Of Pathology, 2011, v. 223 n. 4, p. 496-510 [How to Cite?] DOI: http://dx.doi.org/10.1002/path.2823 |
| dc.identifier.citeulike | 8511490 |
| dc.identifier.doi | http://dx.doi.org/10.1002/path.2823 |
| dc.identifier.epage | 510 |
| dc.identifier.issn | 0022-3417 2011 Impact Factor: 6.318 2011 SCImago Journal Rankings: 0.946 |
| dc.identifier.issue | 4 |
| dc.identifier.pmid | 21294123 |
| dc.identifier.scopus | eid_2-s2.0-79551696483 |
| dc.identifier.spage | 496 |
| dc.identifier.uri | http://hdl.handle.net/10722/163360 |
| dc.identifier.volume | 223 |
| dc.language | eng |
| dc.publisher | John Wiley & Sons. The Journal's web site is located at http://www3.interscience.wiley.com/cgi-bin/jhome/1130 |
| dc.publisher.place | United Kingdom |
| dc.relation.ispartof | Journal of Pathology |
| dc.relation.references | References in Scopus |
| dc.subject.mesh | Adolescent |
| dc.subject.mesh | Adult |
| dc.subject.mesh | Aged |
| dc.subject.mesh | Aged, 80 And Over |
| dc.subject.mesh | Apoptosis - Drug Effects |
| dc.subject.mesh | Female |
| dc.subject.mesh | Gene Expression Profiling - Methods |
| dc.subject.mesh | Gene Regulatory Networks |
| dc.subject.mesh | Genome-Wide Association Study |
| dc.subject.mesh | Humans |
| dc.subject.mesh | Inhibitor Of Apoptosis Proteins |
| dc.subject.mesh | Killer Cells, Natural - Metabolism |
| dc.subject.mesh | Lymphoma, Extranodal Nk-T-Cell - Genetics - Immunology - Metabolism - Pathology |
| dc.subject.mesh | Male |
| dc.subject.mesh | Microtubule-Associated Proteins - Antagonists & Inhibitors - Metabolism - Physiology |
| dc.subject.mesh | Middle Aged |
| dc.subject.mesh | Nf-Kappa B - Metabolism |
| dc.subject.mesh | Neoplasm Proteins - Metabolism |
| dc.subject.mesh | Nordihydroguaiaretic Acid - Analogs & Derivatives - Pharmacology |
| dc.subject.mesh | Nose Neoplasms - Genetics - Immunology - Metabolism - Pathology |
| dc.subject.mesh | Oncogenes - Physiology |
| dc.subject.mesh | Proto-Oncogene Proteins C-Myc - Metabolism |
| dc.subject.mesh | Tumor Cells, Cultured |
| dc.subject.mesh | Tumor Suppressor Protein P53 - Metabolism |
| dc.subject.mesh | Young Adult |
| dc.title | Activated oncogenic pathways and therapeutic targets in extranodal nasal-type NK/T cell lymphoma revealed by gene expression profiling |
| dc.type | Article |
Author Affiliations
- Yong Loo Lin School of Medicine
- Mayo Clinic
- Osaka University
- Toyota Kosei Hospital
- Queen Mary Hospital Hong Kong
- National University of Singapore
- Tokyo Medical and Dental University

