Article: Two novel factor X gene mutations in a Chinese family with factor X deficiency
| Title | Two novel factor X gene mutations in a Chinese family with factor X deficiency |
|---|---|
| Authors | Au, WY1 Lam, CCK2 Cheung, WC1 Kwong, YL1 |
| Issue Date | 2004 |
| Publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/00277/index.htm |
| Citation | Annals Of Hematology, 2004, v. 83 n. 5, p. 304-306 [How to Cite?] DOI: http://dx.doi.org/10.1007/s00277-003-0803-1 |
| Abstract | We report a factor X (FX)-deficient Chinese family with two novel FX gene (F10) mutations. Two sibling probands had a bleeding tendency since childhood. Both had very low FX:C (<0.01 IU/ml) and FX:Ag (5-6%) levels and were heterozygous for two novel F10 mutations, a 2-bp GC deletion involving nucleotides 33 and 34, leading to premature chain termination at residue 45, and a T237→C mutation, leading to Phe71→Ser. A family study confirmed that the mother had the 2-bp GC deletion and a type I FX deficiency. The father had the Phe71→Ser mutation. Interestingly, a type I FX deficiency was also observed, suggesting that Phe71→Ser, occurring at a site sandwiched between two Gla residues, might perturb FX protein stability. © Springer-Verlag 2003. |
| ISSN | 0939-5555 2011 Impact Factor: 2.615 2011 SCImago Journal Rankings: 0.306 |
| DOI | http://dx.doi.org/10.1007/s00277-003-0803-1 |
| References | References in Scopus |
| dc.contributor.author | Au, WY |
|---|---|
| dc.contributor.author | Lam, CCK |
| dc.contributor.author | Cheung, WC |
| dc.contributor.author | Kwong, YL |
| dc.date.accessioned | 2012-09-05T05:24:37Z |
| dc.date.available | 2012-09-05T05:24:37Z |
| dc.date.issued | 2004 |
| dc.description.abstract | We report a factor X (FX)-deficient Chinese family with two novel FX gene (F10) mutations. Two sibling probands had a bleeding tendency since childhood. Both had very low FX:C (<0.01 IU/ml) and FX:Ag (5-6%) levels and were heterozygous for two novel F10 mutations, a 2-bp GC deletion involving nucleotides 33 and 34, leading to premature chain termination at residue 45, and a T237→C mutation, leading to Phe71→Ser. A family study confirmed that the mother had the 2-bp GC deletion and a type I FX deficiency. The father had the Phe71→Ser mutation. Interestingly, a type I FX deficiency was also observed, suggesting that Phe71→Ser, occurring at a site sandwiched between two Gla residues, might perturb FX protein stability. © Springer-Verlag 2003. |
| dc.description.nature | Link_to_subscribed_fulltext |
| dc.identifier.citation | Annals Of Hematology, 2004, v. 83 n. 5, p. 304-306 [How to Cite?] DOI: http://dx.doi.org/10.1007/s00277-003-0803-1 |
| dc.identifier.doi | http://dx.doi.org/10.1007/s00277-003-0803-1 |
| dc.identifier.epage | 306 |
| dc.identifier.issn | 0939-5555 2011 Impact Factor: 2.615 2011 SCImago Journal Rankings: 0.306 |
| dc.identifier.issue | 5 |
| dc.identifier.pmid | 15060750 |
| dc.identifier.scopus | eid_2-s2.0-2342594502 |
| dc.identifier.spage | 304 |
| dc.identifier.uri | http://hdl.handle.net/10722/162872 |
| dc.identifier.volume | 83 |
| dc.language | eng |
| dc.publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/00277/index.htm |
| dc.publisher.place | Germany |
| dc.relation.ispartof | Annals of Hematology |
| dc.relation.references | References in Scopus |
| dc.subject.mesh | Adult |
| dc.subject.mesh | Amino Acid Substitution |
| dc.subject.mesh | Asian Continental Ancestry Group - Genetics |
| dc.subject.mesh | Base Sequence |
| dc.subject.mesh | Blood Coagulation Tests |
| dc.subject.mesh | Cytosine |
| dc.subject.mesh | Factor X - Genetics |
| dc.subject.mesh | Factor X Deficiency - Genetics |
| dc.subject.mesh | Female |
| dc.subject.mesh | Gene Deletion |
| dc.subject.mesh | Guanine |
| dc.subject.mesh | Heterozygote |
| dc.subject.mesh | Humans |
| dc.subject.mesh | Mutation |
| dc.subject.mesh | Pedigree |
| dc.subject.mesh | Phenylalanine |
| dc.subject.mesh | Serine |
| dc.title | Two novel factor X gene mutations in a Chinese family with factor X deficiency |
| dc.type | Article |
Author Affiliations
- The University of Hong Kong
- Queen Mary Hospital Hong Kong

