Article: Mutations in the open reading frame of the β-site APP cleaving enzyme (BACE) locus are not a common cause of Alzheimer's disease
| Title | Mutations in the open reading frame of the β-site APP cleaving enzyme (BACE) locus are not a common cause of Alzheimer's disease |
|---|---|
| Authors | Nicolaou, M7 Song, YQ5 8 Sato, CA5 8 Orlacchio, A9 Kawarai, T5 8 Medeiros, H5 8 Liang, Y5 8 Sorbi, S6 Richard, E5 8 Rogaev, EI5 8 Moliaka, Y1 5 8 Bruni, AC3 Jorge, R2 Percy, M Duara, R4 Farrer, LA7 St GeorgeHyslop, P5 8 Rogaeva, EA1 5 8 |
| Issue Date | 2001 |
| Publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/10048/index.htm |
| Citation | Neurogenetics, 2001, v. 3 n. 4, p. 203-206 [How to Cite?] DOI: http://dx.doi.org/10.1007/s100480100123 |
| Abstract | Amyloid β-peptide (Aβ) plays a central role in the pathogenesis of Alzheimer's disease (AD). The gene encoding the β-site APP cleaving enzyme (BACE), one of two enzymes that sequentially cleave the β-amyloid precursor protein to generate Aβ, has recently been cloned. We tested the hypothesis that BACE might be genetically associated with AD by linkage analysis (56 pedigrees), by direct nucleotide sequencing of the entire open reading frame (20 subjects with familial AD, and 10 subjects with sporadic AD) and by allelic association analysis (155 AD cases and 173 non-demented controls). Our results revealed no evidence for either genetic linkage or allelic association between BACE and AD, and no coding sequence mutations were detected in the open reading frame of the BACE gene. These data suggest that while BACE protein plays an important role in the pathogenesis of AD, and may be a robust therapeutic target, it is unlikely to be a major AD susceptibility locus. © Springer-Verlag 2001. |
| ISSN | 1364-6745 2011 Impact Factor: 3.354 2011 SCImago Journal Rankings: 0.394 |
| DOI | http://dx.doi.org/10.1007/s100480100123 |
| ISI Accession Number ID | WOS:000171833400004 |
| References | References in Scopus |
| dc.contributor.author | Nicolaou, M |
|---|---|
| dc.contributor.author | Song, YQ |
| dc.contributor.author | Sato, CA |
| dc.contributor.author | Orlacchio, A |
| dc.contributor.author | Kawarai, T |
| dc.contributor.author | Medeiros, H |
| dc.contributor.author | Liang, Y |
| dc.contributor.author | Sorbi, S |
| dc.contributor.author | Richard, E |
| dc.contributor.author | Rogaev, EI |
| dc.contributor.author | Moliaka, Y |
| dc.contributor.author | Bruni, AC |
| dc.contributor.author | Jorge, R |
| dc.contributor.author | Percy, M |
| dc.contributor.author | Duara, R |
| dc.contributor.author | Farrer, LA |
| dc.contributor.author | St GeorgeHyslop, P |
| dc.contributor.author | Rogaeva, EA |
| dc.date.accessioned | 2012-05-29T06:03:54Z |
| dc.date.available | 2012-05-29T06:03:54Z |
| dc.date.issued | 2001 |
| dc.description.abstract | Amyloid β-peptide (Aβ) plays a central role in the pathogenesis of Alzheimer's disease (AD). The gene encoding the β-site APP cleaving enzyme (BACE), one of two enzymes that sequentially cleave the β-amyloid precursor protein to generate Aβ, has recently been cloned. We tested the hypothesis that BACE might be genetically associated with AD by linkage analysis (56 pedigrees), by direct nucleotide sequencing of the entire open reading frame (20 subjects with familial AD, and 10 subjects with sporadic AD) and by allelic association analysis (155 AD cases and 173 non-demented controls). Our results revealed no evidence for either genetic linkage or allelic association between BACE and AD, and no coding sequence mutations were detected in the open reading frame of the BACE gene. These data suggest that while BACE protein plays an important role in the pathogenesis of AD, and may be a robust therapeutic target, it is unlikely to be a major AD susceptibility locus. © Springer-Verlag 2001. |
| dc.description.nature | Link_to_subscribed_fulltext |
| dc.identifier.citation | Neurogenetics, 2001, v. 3 n. 4, p. 203-206 [How to Cite?] DOI: http://dx.doi.org/10.1007/s100480100123 |
| dc.identifier.doi | http://dx.doi.org/10.1007/s100480100123 |
| dc.identifier.epage | 206 |
| dc.identifier.hkuros | 69644 |
| dc.identifier.isi | WOS:000171833400004 |
| dc.identifier.issn | 1364-6745 2011 Impact Factor: 3.354 2011 SCImago Journal Rankings: 0.394 |
| dc.identifier.issue | 4 |
| dc.identifier.pmid | 11714100 |
| dc.identifier.scopus | eid_2-s2.0-0035486922 |
| dc.identifier.spage | 203 |
| dc.identifier.uri | http://hdl.handle.net/10722/147463 |
| dc.identifier.volume | 3 |
| dc.language | eng |
| dc.publisher | Springer Verlag. The Journal's web site is located at http://link.springer.de/link/service/journals/10048/index.htm |
| dc.publisher.place | Germany |
| dc.relation.ispartof | Neurogenetics |
| dc.relation.references | References in Scopus |
| dc.subject.mesh | Aged |
| dc.subject.mesh | Aged, 80 And Over |
| dc.subject.mesh | Alzheimer Disease - Genetics |
| dc.subject.mesh | Amyloid Precursor Protein Secretases |
| dc.subject.mesh | Aspartic Acid Endopeptidases - Genetics |
| dc.subject.mesh | Dna Mutational Analysis |
| dc.subject.mesh | Endopeptidases |
| dc.subject.mesh | Genetic Linkage |
| dc.subject.mesh | Genetic Markers |
| dc.subject.mesh | Genotype |
| dc.subject.mesh | Humans |
| dc.subject.mesh | Middle Aged |
| dc.subject.mesh | Mutation |
| dc.subject.mesh | Open Reading Frames - Genetics |
| dc.title | Mutations in the open reading frame of the β-site APP cleaving enzyme (BACE) locus are not a common cause of Alzheimer's disease |
| dc.type | Article |
Author Affiliations
- National Center for Mental Health
- Hospital de Clinicas Jose de San Martin
- Centro Regionale di Neurogenetica ASL 6
- Mount Sinai Medical Center Miami Beach
- University Health Network
- Università degli Studi di Firenze
- Boston University
- University of Toronto
- Fondazione Santa Lucia

