Article: A novel isoform of the 8p22 tumor suppressor gene DLC1 suppresses tumor growth and is frequently silenced in multiple common tumors
| Title | A novel isoform of the 8p22 tumor suppressor gene DLC1 suppresses tumor growth and is frequently silenced in multiple common tumors | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|
| Authors | Low, JSW3 4 Tao, Q3 5 6 Ng, KM6 Goh, HK3 4 Shu, XS6 Woo, WL3 Ambinder, RF3 4 5 Srivastava, G2 Shamay, M3 5 Chan, ATC6 Popescu, NC1 Hsieh, WS3 4 5 | ||||||||||
| Keywords | carcinoma DLC1 methylation p53 RhoGAP tumor suppressor gene | ||||||||||
| Issue Date | 2011 | ||||||||||
| Publisher | Nature Publishing Group. The Journal's web site is located at http://www.nature.com/onc | ||||||||||
| Citation | Oncogene, 2011, v. 30 n. 16, p. 1923-1935 [How to Cite?] DOI: http://dx.doi.org/10.1038/onc.2010.576 | ||||||||||
| Abstract | The critical 8p22 tumor suppressor deleted in liver cancer 1 (DLC1) is frequently inactivated by aberrant CpG methylation and/or genetic deletion and implicated in tumorigeneses of multiple tumor types. Here, we report the identification and characterization of its new isoform, DLC1 isoform 4 (DLC1-i4). This novel isoform encodes an 1125-aa (amino acid) protein with distinct N-terminus as compared with other known DLC1 isoforms. Similar to other isoforms, DLC1-i4 is expressed ubiquitously in normal tissues and immortalized normal epithelial cells, suggesting a role as a major DLC1 transcript. However, differential expression of the four DLC1 isoforms is found in tumor cell lines: Isoform 1 (longest) and 3 (short thus probably nonfunctional) share a promoter and are silenced in almost all cancer and immortalized cell lines, whereas isoform 2 and 4 utilize different promoters and are frequently downregulated. DLC1-i4 is significantly downregulated in multiple carcinoma cell lines, including 2/4 nasopharyngeal, 8/16 (50%) esophageal, 4/16 (25%) gastric, 6/9 (67%) breast, 3/4 colorectal, 4/4 cervical and 2/8(25%) lung carcinoma cell lines. The functional DLC1-i4 promoter is within a CpG island and is activated by wild-type p53. CpG methylation of the DLC1-i4 promoter is associated with its silencing in tumor cells and was detected in 38-100% of multiple primary tumors. Treatment with 5-aza-2′-deoxycytidine or genetic double knockout of DNMT1 and DNMT3B led to demethylation of the promoter and reactivation of its expression, indicating a predominantly epigenetic mechanism of silencing. Ectopic expression of DLC1-i4 in silenced tumor cells strongly inhibited their growth and colony formation. Thus, we identified a new isoform of DLC1 with tumor suppressive function. The differential expression of various DLC1 isoforms suggests interplay in modulating the complex activities of DLC1 during carcinogenesis. © 2011 Macmillan Publishers Limited All rights reserved. | ||||||||||
| ISSN | 0950-9232 2011 Impact Factor: 6.373 2011 SCImago Journal Rankings: 1.216 | ||||||||||
| DOI | http://dx.doi.org/10.1038/onc.2010.576 | ||||||||||
| ISI Accession Number ID | WOS:000289777700008
Funding Information: This project was supported by an A*STAR grant (Johns Hopkins Singapore, QT/WS/RA), a Chinese University of Hong Kong grant (QT) and a grant from Singapore National Research Foundation and the Ministry of Education under the Research Center of Excellence Program (WS/RA). We thank Drs Bert Vogelstein, George Tsao, (Dolly Huang), Michael Obster and Guiyuan Li for some cell lines; and DSMZ (German Collection of Microorganisms & Cell Cultures) for the KYSE cell lines (Shimada et al., Cancer 69: 277-284, 1992). We also thank Drs Wenling Han, Thomas Putti, Luke Tan for some tumor samples. | ||||||||||
| References | References in Scopus |
| dc.contributor.author | Low, JSW | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|
| dc.contributor.author | Tao, Q | ||||||||||
| dc.contributor.author | Ng, KM | ||||||||||
| dc.contributor.author | Goh, HK | ||||||||||
| dc.contributor.author | Shu, XS | ||||||||||
| dc.contributor.author | Woo, WL | ||||||||||
| dc.contributor.author | Ambinder, RF | ||||||||||
| dc.contributor.author | Srivastava, G | ||||||||||
| dc.contributor.author | Shamay, M | ||||||||||
| dc.contributor.author | Chan, ATC | ||||||||||
| dc.contributor.author | Popescu, NC | ||||||||||
| dc.contributor.author | Hsieh, WS | ||||||||||
| dc.date.accessioned | 2011-09-23T06:01:05Z | ||||||||||
| dc.date.available | 2011-09-23T06:01:05Z | ||||||||||
| dc.date.issued | 2011 | ||||||||||
| dc.description.abstract | The critical 8p22 tumor suppressor deleted in liver cancer 1 (DLC1) is frequently inactivated by aberrant CpG methylation and/or genetic deletion and implicated in tumorigeneses of multiple tumor types. Here, we report the identification and characterization of its new isoform, DLC1 isoform 4 (DLC1-i4). This novel isoform encodes an 1125-aa (amino acid) protein with distinct N-terminus as compared with other known DLC1 isoforms. Similar to other isoforms, DLC1-i4 is expressed ubiquitously in normal tissues and immortalized normal epithelial cells, suggesting a role as a major DLC1 transcript. However, differential expression of the four DLC1 isoforms is found in tumor cell lines: Isoform 1 (longest) and 3 (short thus probably nonfunctional) share a promoter and are silenced in almost all cancer and immortalized cell lines, whereas isoform 2 and 4 utilize different promoters and are frequently downregulated. DLC1-i4 is significantly downregulated in multiple carcinoma cell lines, including 2/4 nasopharyngeal, 8/16 (50%) esophageal, 4/16 (25%) gastric, 6/9 (67%) breast, 3/4 colorectal, 4/4 cervical and 2/8(25%) lung carcinoma cell lines. The functional DLC1-i4 promoter is within a CpG island and is activated by wild-type p53. CpG methylation of the DLC1-i4 promoter is associated with its silencing in tumor cells and was detected in 38-100% of multiple primary tumors. Treatment with 5-aza-2′-deoxycytidine or genetic double knockout of DNMT1 and DNMT3B led to demethylation of the promoter and reactivation of its expression, indicating a predominantly epigenetic mechanism of silencing. Ectopic expression of DLC1-i4 in silenced tumor cells strongly inhibited their growth and colony formation. Thus, we identified a new isoform of DLC1 with tumor suppressive function. The differential expression of various DLC1 isoforms suggests interplay in modulating the complex activities of DLC1 during carcinogenesis. © 2011 Macmillan Publishers Limited All rights reserved. | ||||||||||
| dc.description.nature | Link_to_subscribed_fulltext | ||||||||||
| dc.identifier.citation | Oncogene, 2011, v. 30 n. 16, p. 1923-1935 [How to Cite?] DOI: http://dx.doi.org/10.1038/onc.2010.576 | ||||||||||
| dc.identifier.citeulike | 8623372 | ||||||||||
| dc.identifier.doi | http://dx.doi.org/10.1038/onc.2010.576 | ||||||||||
| dc.identifier.epage | 1935 | ||||||||||
| dc.identifier.hkuros | 184387 | ||||||||||
| dc.identifier.isi | WOS:000289777700008
Funding Information: This project was supported by an A*STAR grant (Johns Hopkins Singapore, QT/WS/RA), a Chinese University of Hong Kong grant (QT) and a grant from Singapore National Research Foundation and the Ministry of Education under the Research Center of Excellence Program (WS/RA). We thank Drs Bert Vogelstein, George Tsao, (Dolly Huang), Michael Obster and Guiyuan Li for some cell lines; and DSMZ (German Collection of Microorganisms & Cell Cultures) for the KYSE cell lines (Shimada et al., Cancer 69: 277-284, 1992). We also thank Drs Wenling Han, Thomas Putti, Luke Tan for some tumor samples. | ||||||||||
| dc.identifier.issn | 0950-9232 2011 Impact Factor: 6.373 2011 SCImago Journal Rankings: 1.216 | ||||||||||
| dc.identifier.issue | 16 | ||||||||||
| dc.identifier.openurl | ![]() | ||||||||||
| dc.identifier.pmid | 21217778 | ||||||||||
| dc.identifier.scopus | eid_2-s2.0-79955466717 | ||||||||||
| dc.identifier.spage | 1923 | ||||||||||
| dc.identifier.uri | http://hdl.handle.net/10722/139913 | ||||||||||
| dc.identifier.volume | 30 | ||||||||||
| dc.language | eng | ||||||||||
| dc.publisher | Nature Publishing Group. The Journal's web site is located at http://www.nature.com/onc | ||||||||||
| dc.publisher.place | United Kingdom | ||||||||||
| dc.relation.ispartof | Oncogene | ||||||||||
| dc.relation.references | References in Scopus | ||||||||||
| dc.subject.mesh | Chromosomes, Human, Pair 8 | ||||||||||
| dc.subject.mesh | GTPase-Activating Proteins - genetics | ||||||||||
| dc.subject.mesh | Genes, Tumor Suppressor | ||||||||||
| dc.subject.mesh | Neoplasms - genetics - pathology | ||||||||||
| dc.subject.mesh | Tumor Suppressor Proteins - genetics | ||||||||||
| dc.subject | carcinoma | ||||||||||
| dc.subject | DLC1 | ||||||||||
| dc.subject | methylation | ||||||||||
| dc.subject | p53 | ||||||||||
| dc.subject | RhoGAP | ||||||||||
| dc.subject | tumor suppressor gene | ||||||||||
| dc.title | A novel isoform of the 8p22 tumor suppressor gene DLC1 suppresses tumor growth and is frequently silenced in multiple common tumors | ||||||||||
| dc.type | Article |
- National Cancer Institute
- The University of Hong Kong
- Johns Hopkins Singapore
- National University of Singapore
- The Johns Hopkins School of Medicine
- Chinese University of Hong Kong


