Article: Reduced transverse relaxation rate (RR2) for improved sensitivity in monitoring myocardial iron in thalassemia
| Title | Reduced transverse relaxation rate (RR2) for improved sensitivity in monitoring myocardial iron in thalassemia |
|---|---|
| Authors | Cheung, JS Au, WY Ha, SY Kim, D Jensen, JH Zhou, IY Cheung, MM Wu, Y Guo, H Khong, PL Brown, TR Brittenham, GM Wu, EX |
| Keywords | cardiac MR chelation therapy ferritin heart hemosiderin iron overload MRI RR2 thalassemia |
| Issue Date | 2011 |
| Publisher | John Wiley & Sons, Inc. The Journal's web site is located at http://www.interscience.wiley.com/jpages/1053-1807/ |
| Citation | Journal Of Magnetic Resonance Imaging, 2011, v. 33 n. 6, p. 1510-1516 [How to Cite?] DOI: http://dx.doi.org/10.1002/jmri.22553 |
| Abstract | Purpose: To evaluate the reduced transverse relaxation rate (RR2), a new relaxation index which has been shown recently to be primarily sensitive to intracellular ferritin iron, as a means of detecting short-term changes in myocardial storage iron produced by iron-chelating therapy in transfusion-dependent thalassemia patients. Materials and Methods: A single-breathhold multi-echo fast spin-echo sequence was implemented at 3 Tesla (T) to estimate RR2 by acquiring signal decays with interecho times of 5, 9 and 13 ms. Transfusion-dependent thalassemia patients (N = 8) were examined immediately before suspending iron-chelating therapy for 1 week (Day 0), after a 1-week suspension of chelation (Day 7), and after a 1-week resumption of chelation (Day 14). Results: The mean percent changes in RR2, R2, and R2* off chelation (between Day 0 and 7) were 11.9 ± 8.9%, 5.4 ± 7.7% and -4.4 ± 25.0%; and, after resuming chelation (between Day 7 and 14), -10.6 ± 13.9%, -8.9 ± 8.0% and -8.5 ± 24.3%, respectively. Significant differences in R2 and RR2 were observed between Day 0 and 7, and between Day 7 and 14, with the greatest proportional changes in RR2. No significant differences in R2* were found. Conclusion: These initial results demonstrate that significant differences in RR2 are detectable after a single week of changes in iron-chelating therapy, likely as a result of superior sensitivity to soluble ferritin iron, which is in close equilibrium with the chelatable cytosolic iron pool. RR2 measurement may provide a new means of monitoring the short-term effectiveness of iron-chelating agents in patients with myocardial iron overload. Copyright © 2011 Wiley-Liss, Inc. |
| ISSN | 1053-1807 2011 Impact Factor: 2.698 2011 SCImago Journal Rankings: 0.242 |
| DOI | http://dx.doi.org/10.1002/jmri.22553 |
| PubMed Central ID | PMC3098046 |
| References | References in Scopus |
| dc.contributor.author | Cheung, JS | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|
| dc.contributor.author | Au, WY | ||||||||||
| dc.contributor.author | Ha, SY | ||||||||||
| dc.contributor.author | Kim, D | ||||||||||
| dc.contributor.author | Jensen, JH | ||||||||||
| dc.contributor.author | Zhou, IY | ||||||||||
| dc.contributor.author | Cheung, MM | ||||||||||
| dc.contributor.author | Wu, Y | ||||||||||
| dc.contributor.author | Guo, H | ||||||||||
| dc.contributor.author | Khong, PL | ||||||||||
| dc.contributor.author | Brown, TR | ||||||||||
| dc.contributor.author | Brittenham, GM | ||||||||||
| dc.contributor.author | Wu, EX | ||||||||||
| dc.date.accessioned | 2011-09-23T05:45:34Z | ||||||||||
| dc.date.available | 2011-09-23T05:45:34Z | ||||||||||
| dc.date.issued | 2011 | ||||||||||
| dc.description.abstract | Purpose: To evaluate the reduced transverse relaxation rate (RR2), a new relaxation index which has been shown recently to be primarily sensitive to intracellular ferritin iron, as a means of detecting short-term changes in myocardial storage iron produced by iron-chelating therapy in transfusion-dependent thalassemia patients. Materials and Methods: A single-breathhold multi-echo fast spin-echo sequence was implemented at 3 Tesla (T) to estimate RR2 by acquiring signal decays with interecho times of 5, 9 and 13 ms. Transfusion-dependent thalassemia patients (N = 8) were examined immediately before suspending iron-chelating therapy for 1 week (Day 0), after a 1-week suspension of chelation (Day 7), and after a 1-week resumption of chelation (Day 14). Results: The mean percent changes in RR2, R2, and R2* off chelation (between Day 0 and 7) were 11.9 ± 8.9%, 5.4 ± 7.7% and -4.4 ± 25.0%; and, after resuming chelation (between Day 7 and 14), -10.6 ± 13.9%, -8.9 ± 8.0% and -8.5 ± 24.3%, respectively. Significant differences in R2 and RR2 were observed between Day 0 and 7, and between Day 7 and 14, with the greatest proportional changes in RR2. No significant differences in R2* were found. Conclusion: These initial results demonstrate that significant differences in RR2 are detectable after a single week of changes in iron-chelating therapy, likely as a result of superior sensitivity to soluble ferritin iron, which is in close equilibrium with the chelatable cytosolic iron pool. RR2 measurement may provide a new means of monitoring the short-term effectiveness of iron-chelating agents in patients with myocardial iron overload. Copyright © 2011 Wiley-Liss, Inc. | ||||||||||
| dc.description.nature | link_to_OA_fulltext | ||||||||||
| dc.identifier.citation | Journal Of Magnetic Resonance Imaging, 2011, v. 33 n. 6, p. 1510-1516 [How to Cite?] DOI: http://dx.doi.org/10.1002/jmri.22553 | ||||||||||
| dc.identifier.doi | http://dx.doi.org/10.1002/jmri.22553 | ||||||||||
| dc.identifier.epage | 1516 | ||||||||||
| dc.identifier.hkuros | 192054 | ||||||||||
| dc.identifier.isi | WOS:000291267700028
Funding Information: Contract grant sponsor: Hong Kong Research Grant Council; Contract grant number: GRF7794/07M; Contract grant sponsor: Hong Kong Children Thalassaemia Foundation; Contract grant number: 2007/02; Contract grant sponsor: National Institutes of Health; Contract grant numbers: R01-DK069373, R01-DK066251, R37-DK049108, R01-DK049108; Contract grant sponsor: American Heart Association; Contract grant number: 0730143N. | ||||||||||
| dc.identifier.issn | 1053-1807 2011 Impact Factor: 2.698 2011 SCImago Journal Rankings: 0.242 | ||||||||||
| dc.identifier.issue | 6 | ||||||||||
| dc.identifier.pmcid | PMC3098046 | ||||||||||
| dc.identifier.pmid | 21591022 | ||||||||||
| dc.identifier.scopus | eid_2-s2.0-79958254314 | ||||||||||
| dc.identifier.spage | 1510 | ||||||||||
| dc.identifier.uri | http://hdl.handle.net/10722/139127 | ||||||||||
| dc.identifier.volume | 33 | ||||||||||
| dc.language | eng | ||||||||||
| dc.publisher | John Wiley & Sons, Inc. The Journal's web site is located at http://www.interscience.wiley.com/jpages/1053-1807/ | ||||||||||
| dc.publisher.place | United States | ||||||||||
| dc.relation.ispartof | Journal of Magnetic Resonance Imaging | ||||||||||
| dc.relation.references | References in Scopus | ||||||||||
| dc.rights | Journal of Magnetic Resonance Imaging. Copyright © John Wiley & Sons, Inc. | ||||||||||
| dc.subject.mesh | Blood Transfusion | ||||||||||
| dc.subject.mesh | Chelating Agents - pharmacology | ||||||||||
| dc.subject.mesh | Iron - chemistry | ||||||||||
| dc.subject.mesh | Myocardium - pathology | ||||||||||
| dc.subject.mesh | Thalassemia - diagnosis - pathology | ||||||||||
| dc.subject | cardiac MR | ||||||||||
| dc.subject | chelation therapy | ||||||||||
| dc.subject | ferritin | ||||||||||
| dc.subject | heart | ||||||||||
| dc.subject | hemosiderin | ||||||||||
| dc.subject | iron overload | ||||||||||
| dc.subject | MRI | ||||||||||
| dc.subject | RR2 | ||||||||||
| dc.subject | thalassemia | ||||||||||
| dc.title | Reduced transverse relaxation rate (RR2) for improved sensitivity in monitoring myocardial iron in thalassemia | ||||||||||
| dc.type | Article |
Author Affiliations
- Massachusetts General Hospital
- New York University School of Medicine
- Columbia University in the City of New York
- The University of Hong Kong
- Columbia University, College of Physicians and Surgeons
- Tsinghua University

