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Article: Kbg syndrome: Clinical features and specific dental findings

TitleKbg syndrome: Clinical features and specific dental findings
Authors
KeywordsKbg syndrome
Macrodontic Incisor
Supernumerary
Talon cusp
Tooth
Words
Issue Date2010
PublisherAmerican Academy of Pediatric Dentistry. The Journal's web site is located at http://www.aapd.org/publications/peddent/
Citation
Pediatric Dentistry, 2010, v. 32 n. 5, p. 439-444 How to Cite?
AbstractPurpose: This investigation sought to identify the common manifestations of KBG syndrome in the literature and to determine the major oral abnormalities in a 12-year-old Chinese boy. Methods: PUBMED search, using the keyword phrase "KBG syndrome," produced 20 articles. Due to the disparities in the quality of evaluations in the reports, any physical feature that was not discussed was assumed to be absent. Results: Of the 54 cases, including the present case, 36 (67%) were males. Mental retardation or global developmental delay was reported in 42 (78%) cases, while 46 (85%) exhibited shortness of stature. Oral features occurred in 53 (98%) cases; macrodontia was present in 49 (96%) cases; the present case was the only one with hyperdontia and a talon cusp. Other features were craniofacial anomalies, followed by abnormalities of the nose, hand, mouth, eyes, eyebrows, philtrum, costovertebrae, ears, and, less frequently, low hairline and lower extremity abnormalities. Conclusions: Cardinal features of KBG syndrome include facial dysmorphism, short stature, skeletal anomalies, and mild developmental delay; intraorally, macrodontia of the maxillary central incisors occurs in most cases. This is the first known report of KBG syndrome in a Chinese subject and the only case with hyperdontia and a talon cusp.
Persistent Identifierhttp://hdl.handle.net/10722/129066
ISSN
2015 Impact Factor: 0.872
2015 SCImago Journal Rankings: 0.458
ISI Accession Number ID
References

 

DC FieldValueLanguage
dc.contributor.authorAlmandey, HAen_HK
dc.contributor.authorAnthonappa, RPen_HK
dc.contributor.authorKing, NMen_HK
dc.contributor.authorFung, CWen_HK
dc.date.accessioned2010-12-23T08:32:02Z-
dc.date.available2010-12-23T08:32:02Z-
dc.date.issued2010en_HK
dc.identifier.citationPediatric Dentistry, 2010, v. 32 n. 5, p. 439-444en_HK
dc.identifier.issn0164-1263en_HK
dc.identifier.urihttp://hdl.handle.net/10722/129066-
dc.description.abstractPurpose: This investigation sought to identify the common manifestations of KBG syndrome in the literature and to determine the major oral abnormalities in a 12-year-old Chinese boy. Methods: PUBMED search, using the keyword phrase "KBG syndrome," produced 20 articles. Due to the disparities in the quality of evaluations in the reports, any physical feature that was not discussed was assumed to be absent. Results: Of the 54 cases, including the present case, 36 (67%) were males. Mental retardation or global developmental delay was reported in 42 (78%) cases, while 46 (85%) exhibited shortness of stature. Oral features occurred in 53 (98%) cases; macrodontia was present in 49 (96%) cases; the present case was the only one with hyperdontia and a talon cusp. Other features were craniofacial anomalies, followed by abnormalities of the nose, hand, mouth, eyes, eyebrows, philtrum, costovertebrae, ears, and, less frequently, low hairline and lower extremity abnormalities. Conclusions: Cardinal features of KBG syndrome include facial dysmorphism, short stature, skeletal anomalies, and mild developmental delay; intraorally, macrodontia of the maxillary central incisors occurs in most cases. This is the first known report of KBG syndrome in a Chinese subject and the only case with hyperdontia and a talon cusp.en_HK
dc.languageengen_US
dc.publisherAmerican Academy of Pediatric Dentistry. The Journal's web site is located at http://www.aapd.org/publications/peddent/en_HK
dc.relation.ispartofPediatric Dentistryen_HK
dc.subjectKbg syndromeen_HK
dc.subjectMacrodontic Incisoren_HK
dc.subjectSupernumeraryen_HK
dc.subjectTalon cuspen_HK
dc.subjectToothen_HK
dc.subjectWordsen_HK
dc.subject.meshAbnormalities, Multiple-
dc.subject.meshBone Diseases, Developmental - complications-
dc.subject.meshCraniofacial Abnormalities - complications-
dc.subject.meshIncisor - abnormalities-
dc.subject.meshTooth Abnormalities - complications - etiology-
dc.titleKbg syndrome: Clinical features and specific dental findingsen_HK
dc.typeArticleen_HK
dc.identifier.openurlhttp://library.hku.hk:4550/resserv?sid=HKU:IR&issn=0164-1263&volume=32&issue=5&spage=439&epage=444&date=2010&atitle=KBG+Syndrome:+Clinical+features+and+specific+dental+findings-
dc.identifier.emailKing, NM: hhdbknm@hkucc.hku.hken_HK
dc.identifier.authorityKing, NM=rp00006en_HK
dc.description.naturelink_to_subscribed_fulltext-
dc.identifier.pmid21070713-
dc.identifier.scopuseid_2-s2.0-79952110803en_HK
dc.identifier.hkuros183291en_US
dc.relation.referenceshttp://www.scopus.com/mlt/select.url?eid=2-s2.0-79952110803&selection=ref&src=s&origin=recordpageen_HK
dc.identifier.volume32en_HK
dc.identifier.issue5en_HK
dc.identifier.spage439en_HK
dc.identifier.epage444en_HK
dc.identifier.isiWOS:000287634900011-
dc.publisher.placeUnited Statesen_HK
dc.identifier.scopusauthoridAlmandey, HA=39061136000en_HK
dc.identifier.scopusauthoridAnthonappa, RP=16241017100en_HK
dc.identifier.scopusauthoridKing, NM=7201762850en_HK
dc.identifier.scopusauthoridFung, CW=37000455500en_HK

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