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Article: Primitive neuroectodermal adrenal gland tumour

TitlePrimitive neuroectodermal adrenal gland tumour
Authors
Issue Date2014
PublisherHong Kong Academy of Medicine Press. The Journal's web site is located at http://www.hkmj.org.hk
Citation
Hong Kong Medical Journal, 2014, v. 20 n. 5, p. 444-446 How to Cite?
AbstractEwing's sarcoma, also called primitive neuroectodermal tumour of the adrenal gland, is extremely rare. Only a few cases have been reported in the literature. We report on a woman with adult-onset primitive neuroectodermal tumour of the adrenal gland presenting with progressive flank pain. Computed tomography confirmed an adrenal tumour with invasion of the left diaphragm and kidney. Radical surgery was performed and the pain completely resolved; histology confirmed the presence of primitive neuroectodermal tumour, for which she was given chemotherapy. The clinical presentation of this condition is non-specific, and a definitive diagnosis is based on a combination of histology, as well as immunohistochemical and cytogenic analysis. According to the literature, these tumours demonstrate rapid growth and aggressive behaviour but there are no well-established guidelines or treatment strategies. Nevertheless, surgery remains the mainstay of local disease control; curative surgery can be performed in most patients. Adjuvant chemoirradiation has been advocated yet no consensus is available. The prognosis of patients with primitive neuroectodermal tumours remains poor.
Persistent Identifierhttp://hdl.handle.net/10722/206829
ISSN
2015 Impact Factor: 0.887
2015 SCImago Journal Rankings: 0.279

 

DC FieldValueLanguage
dc.contributor.authorTsang, YP-
dc.contributor.authorLang, BHH-
dc.contributor.authorTam, SC-
dc.contributor.authorWong, KP-
dc.date.accessioned2014-12-02T10:06:02Z-
dc.date.available2014-12-02T10:06:02Z-
dc.date.issued2014-
dc.identifier.citationHong Kong Medical Journal, 2014, v. 20 n. 5, p. 444-446-
dc.identifier.issn1024-2708-
dc.identifier.urihttp://hdl.handle.net/10722/206829-
dc.description.abstractEwing's sarcoma, also called primitive neuroectodermal tumour of the adrenal gland, is extremely rare. Only a few cases have been reported in the literature. We report on a woman with adult-onset primitive neuroectodermal tumour of the adrenal gland presenting with progressive flank pain. Computed tomography confirmed an adrenal tumour with invasion of the left diaphragm and kidney. Radical surgery was performed and the pain completely resolved; histology confirmed the presence of primitive neuroectodermal tumour, for which she was given chemotherapy. The clinical presentation of this condition is non-specific, and a definitive diagnosis is based on a combination of histology, as well as immunohistochemical and cytogenic analysis. According to the literature, these tumours demonstrate rapid growth and aggressive behaviour but there are no well-established guidelines or treatment strategies. Nevertheless, surgery remains the mainstay of local disease control; curative surgery can be performed in most patients. Adjuvant chemoirradiation has been advocated yet no consensus is available. The prognosis of patients with primitive neuroectodermal tumours remains poor.-
dc.languageeng-
dc.publisherHong Kong Academy of Medicine Press. The Journal's web site is located at http://www.hkmj.org.hk-
dc.relation.ispartofHong Kong Medical Journal-
dc.rightsHong Kong Medical Journal. Copyright © Hong Kong Academy of Medicine Press.-
dc.rightsCreative Commons: Attribution 3.0 Hong Kong License-
dc.titlePrimitive neuroectodermal adrenal gland tumour-
dc.typeArticle-
dc.identifier.emailLang, BHH: Blang@hku.hk-
dc.identifier.authorityLang, HHB=rp01828en_US
dc.description.naturepublished_or_final_version-
dc.identifier.doi10.12809/hkmj134127-
dc.identifier.pmid25307073-
dc.identifier.hkuros241417-
dc.identifier.volume20-
dc.identifier.issue5-
dc.identifier.spage444-
dc.identifier.epage446-
dc.publisher.placeHong Kong-

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