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Article: Takayasu's arteritis associated with Wiskott-Aldrich syndrome

TitleTakayasu's arteritis associated with Wiskott-Aldrich syndrome
Authors
Issue Date1992
PublisherBlackwell Publishing Asia. The Journal's web site is located at http://www.blackwellpublishing.com/journals/JPC
Citation
Journal Of Paediatrics And Child Health, 1992, v. 28 n. 5, p. 407-409 How to Cite?
AbstractA unique case of a Chinese boy with Wiskott-Aldrich syndrome (WAS) associated with Takayasu's arteritis is reported. He had eczema, epistaxis and recurrent infections since early infancy and was found to have thrombocytopenia, negative delayed-type skin hypersensitivity, low T cell number and impaired lymphocyte proliferation to phytohaemagglutinin and concanavalin A. He had high normal serum immunoglobulin (Ig)G and IgA with low IgM and isohaemagglutinin. He presented with hypertensive encephalopathy at 5.5 years of age and an aortogram demonstrated abdominal aortic aneurysm with bilateral stenosis of renal arteries resulting in renovascular hypertension. His hypertension was difficult to control medically and autotransplant of his kidneys to the iliac arteries was performed, but he died in the immediate postoperative period. The relationship between immunodeficiency and collagen-vascular disease was discussed.
Persistent Identifierhttp://hdl.handle.net/10722/170250
ISSN
2015 Impact Factor: 1.477
2015 SCImago Journal Rankings: 0.692
ISI Accession Number ID

 

DC FieldValueLanguage
dc.contributor.authorLau, YLen_US
dc.contributor.authorWong, SNen_US
dc.contributor.authorLawton, WMen_US
dc.date.accessioned2012-10-30T06:06:58Z-
dc.date.available2012-10-30T06:06:58Z-
dc.date.issued1992en_US
dc.identifier.citationJournal Of Paediatrics And Child Health, 1992, v. 28 n. 5, p. 407-409en_US
dc.identifier.issn1034-4810en_US
dc.identifier.urihttp://hdl.handle.net/10722/170250-
dc.description.abstractA unique case of a Chinese boy with Wiskott-Aldrich syndrome (WAS) associated with Takayasu's arteritis is reported. He had eczema, epistaxis and recurrent infections since early infancy and was found to have thrombocytopenia, negative delayed-type skin hypersensitivity, low T cell number and impaired lymphocyte proliferation to phytohaemagglutinin and concanavalin A. He had high normal serum immunoglobulin (Ig)G and IgA with low IgM and isohaemagglutinin. He presented with hypertensive encephalopathy at 5.5 years of age and an aortogram demonstrated abdominal aortic aneurysm with bilateral stenosis of renal arteries resulting in renovascular hypertension. His hypertension was difficult to control medically and autotransplant of his kidneys to the iliac arteries was performed, but he died in the immediate postoperative period. The relationship between immunodeficiency and collagen-vascular disease was discussed.en_US
dc.languageengen_US
dc.publisherBlackwell Publishing Asia. The Journal's web site is located at http://www.blackwellpublishing.com/journals/JPCen_US
dc.relation.ispartofJournal of Paediatrics and Child Healthen_US
dc.subject.meshChild, Preschoolen_US
dc.subject.meshHumansen_US
dc.subject.meshMaleen_US
dc.subject.meshTakayasu Arteritis - Complications - Immunologyen_US
dc.subject.meshWiskott-Aldrich Syndrome - Complications - Immunologyen_US
dc.titleTakayasu's arteritis associated with Wiskott-Aldrich syndromeen_US
dc.typeArticleen_US
dc.identifier.emailLau, YL:lauylung@hkucc.hku.hken_US
dc.identifier.authorityLau, YL=rp00361en_US
dc.description.naturelink_to_subscribed_fulltexten_US
dc.identifier.doi10.1111/j.1440-1754.1992.tb02703.x-
dc.identifier.pmid1356386-
dc.identifier.scopuseid_2-s2.0-0026447796en_US
dc.identifier.volume28en_US
dc.identifier.issue5en_US
dc.identifier.spage407en_US
dc.identifier.epage409en_US
dc.identifier.isiWOS:A1992JR56400016-
dc.publisher.placeAustraliaen_US
dc.identifier.scopusauthoridLau, YL=7201403380en_US
dc.identifier.scopusauthoridWong, SN=7404590305en_US
dc.identifier.scopusauthoridLawton, WM=7007016909en_US

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